debranching enzyme
Starch structure modifier
A debranching enzyme is a protein that removes branch points from complex carbohydrates, particularly glycogen and starch.
These branched molecules store energy efficiently but require debranching enzymes to release glucose units at fork points during digestion or metabolism.
Deficiency in glycogen debranching enzyme causes a metabolic disorder called glycogen storage disease type III.
- glycogenStored glucose polymer
- starchComplex plant carbohydrate
- hydrolysisWater-induced bond cleavage
- glucosePrimary cellular fuel
- maltoseTwo-glucose disaccharide
catalysis · substrate · liver · muscle · metabolism · carbohydrate · dextrin · cleaving · breaking · breaking down · storage · energy · energy release · digestion · polymer · chain · linkage · fermentation
- RNA splicingpre-mRNA, intron, exon, alternative splicing, introns
- glycogen metabolismUDP-glucose
- RNA machineryribosome, dicer
- amylasesamylase, alpha-amylase, diastase